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Підшкірна паннікулітоподібна Т-клітинна лімфома

ORPHA:86884· ICD-10 C86.3· Subcutaneous panniculitis-like T-cell lymphoma

Визначення(English summary)

A rare cytotoxic cutaneous alpha-beta T-cell lymphoma characterized by solitary or multiple erythematous subcutaneous nodules and plaques that can be localized to the lower extremities or generalized. It has been recognized as a distinct subset of peripheral T-cell lymphomas originating and presenting primarily in the subcutaneous fat tissue and often associated with hemophagocytic lymphohistiocytosis.

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
All ages