Subcutaneous panniculitis-like T-cell lymphoma
ORPHA:86884· ICD-10 C86.3
Definition
A rare cytotoxic cutaneous alpha-beta T-cell lymphoma characterized by solitary or multiple erythematous subcutaneous nodules and plaques that can be localized to the lower extremities or generalized. It has been recognized as a distinct subset of peripheral T-cell lymphomas originating and presenting primarily in the subcutaneous fat tissue and often associated with hemophagocytic lymphohistiocytosis.
- Prevalence
- Unknown
- Inheritance
- Not applicable
- Age of onset
- All ages