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Subcutaneous panniculitis-like T-cell lymphoma

ORPHA:86884· ICD-10 C86.3

Definition

A rare cytotoxic cutaneous alpha-beta T-cell lymphoma characterized by solitary or multiple erythematous subcutaneous nodules and plaques that can be localized to the lower extremities or generalized. It has been recognized as a distinct subset of peripheral T-cell lymphomas originating and presenting primarily in the subcutaneous fat tissue and often associated with hemophagocytic lymphohistiocytosis.

Prevalence
Unknown
Inheritance
Not applicable
Age of onset
All ages