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Вузлова маргінальна В-клітинна лімфома

ORPHA:86867· ICD-10 C83.0· Nodal marginal zone B-cell lymphoma

Визначення(English summary)

Nodal marginal zone B-cell lymphoma is a rare, indolent B-cell non-Hodgkin lymphoma, characterized by abnormal clonal proliferation of mature B-lymphocytes with involvement of the lymph nodes, sometimes the bone marrow, and rarely the blood. Clinically it presents with disseminated peripheral, abdominal and/or thoracic lymphadenopathy. Cytopenia and bulky tumors (greater than 5 cm) are rare. Association with Hepatitis C virus and chronic inflammation has been reported.

Поширеність
1-9 / 100 000
Успадкування
Not applicable
Вік початку
Adolescent, Adult, Elderly