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Хронічне мієлопроліферативне захворювання, не класифіковане

ORPHA:86830· ICD-10 D47.1· Chronic myeloproliferative disease, unclassifiable

Визначення(English summary)

A rare hematological neoplasm characterized by clonal proliferation of myeloid precursors in the bone marrow, blood and other tissues (spleen, liver), with clinical, morphological and molecular features ofmyeloproliferative neoplasms (MPN), failing to meet criteria of a specific MPN. The presentation is nonspecific and variable and often includes leukocytosis, thrombocytosis and anemia. Splenomegaly, hepatomegaly as well as fatigue, malaise or weight loss may appear in advanced stages.

Поширеність
1-9 / 1 000 000
Вік початку
Adult