Хвороба Старгардта
ORPHA:827· ICD-10 H35.5· Stargardt disease
Визначення(English summary)
A rare ophthalmic disorder that is usually characterized by a progressive loss of central vision associated with irregular macular and perimacular yellow-white fundus flecks, and a so-called ''beaten bronze'' atrophic central macular lesion.
- Поширеність
- 1-5 / 10 000
- Успадкування
- Autosomal dominant, Autosomal recessive
- Вік початку
- Adolescent, Adult, Childhood, Elderly