Спадкова папілярна нирковоклітинна карцинома
ORPHA:47044· ICD-10 C64· Hereditary papillary renal cell carcinoma
Визначення(English summary)
A rare familial renal cancer syndrome characterized by a predisposition for developing bilateral and multifocal classic type papillary renal cell carcinomas (formerly known as type 1 papillary renal cell carcinoma until the 2022 WHO classification of renal tumors).
- Успадкування
- Autosomal dominant
- Вік початку
- Adult