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Спадкова папілярна нирковоклітинна карцинома

ORPHA:47044· ICD-10 C64· Hereditary papillary renal cell carcinoma

Визначення(English summary)

A rare familial renal cancer syndrome characterized by a predisposition for developing bilateral and multifocal classic type papillary renal cell carcinomas (formerly known as type 1 papillary renal cell carcinoma until the 2022 WHO classification of renal tumors).

Успадкування
Autosomal dominant
Вік початку
Adult