Hereditary papillary renal cell carcinoma
ORPHA:47044· ICD-10 C64
Definition
A rare familial renal cancer syndrome characterized by a predisposition for developing bilateral and multifocal classic type papillary renal cell carcinomas (formerly known as type 1 papillary renal cell carcinoma until the 2022 WHO classification of renal tumors).
- Inheritance
- Autosomal dominant
- Age of onset
- Adult