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Анти-p200 пемфігоїд

ORPHA:454710· ICD-10 L12.8· Anti-p200 pemphigoid

Визначення(English summary)

A rare, acquired, subepidermal autoimmune bullous disease characterized by polymorphic cutaneous lesions (blisters, urticarial lesions or scars/milia) associated with imunoglubulin G deposition in the basement membrane zone. Lesions are frequently localized on extremities, trunk, palmoplantar and cephalic areas as well as mucous membranes.

Поширеність
<1 / 1 000 000
Успадкування
Not applicable
Вік початку
Adult, Elderly