Анти-p200 пемфігоїд
ORPHA:454710· ICD-10 L12.8· Anti-p200 pemphigoid
Визначення(English summary)
A rare, acquired, subepidermal autoimmune bullous disease characterized by polymorphic cutaneous lesions (blisters, urticarial lesions or scars/milia) associated with imunoglubulin G deposition in the basement membrane zone. Lesions are frequently localized on extremities, trunk, palmoplantar and cephalic areas as well as mucous membranes.
- Поширеність
- <1 / 1 000 000
- Успадкування
- Not applicable
- Вік початку
- Adult, Elderly