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С3 гломерулопатія

ORPHA:329918· ICD-10 N03.5· C3 glomerulopathy

Визначення(English summary)

A form of primary membranoproliferative glomerulonephritis characterized by the presence in renal biopsy samples of a glomerulonephritis with sole (or at least dominant) glomerular immunofluorescence staining for C3. Non-specific alterations or proliferative patterns with C3-dominant glomerular staining are also possible. Based upon electron microscopic findings, C3 glomerulopathy (C3G) may be further classified as C3 glomerulonephritis (C3GN) or Dense deposit disease (DDD).

Поширеність
1-9 / 1 000 000
Успадкування
Multigenic/multifactorial
Вік початку
All ages