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Синдром POEMS

ORPHA:2905· ICD-10 D47.2· POEMS syndrome

Визначення(English summary)

POEMS syndrome is a paraneoplastic syndrome characterized by polyradiculoneuropathy (P), organomegaly (O), endocrinopathy (E), clonal plasma cell disorder (M), and skin changes (S). Other features include papilledema, extravascular volume overload, sclerotic bone lesions, thrombocytosis/erythrocytosis, and elevated VEGF levels.

Поширеність
1-9 / 1 000 000
Успадкування
Unknown
Вік початку
Adult, Elderly