POEMS syndrome
ORPHA:2905· ICD-10 D47.2
Definition
POEMS syndrome is a paraneoplastic syndrome characterized by polyradiculoneuropathy (P), organomegaly (O), endocrinopathy (E), clonal plasma cell disorder (M), and skin changes (S). Other features include papilledema, extravascular volume overload, sclerotic bone lesions, thrombocytosis/erythrocytosis, and elevated VEGF levels.
- Prevalence
- 1-9 / 1 000 000
- Inheritance
- Unknown
- Age of onset
- Adult, Elderly