Бульозний дифузний шкірний мастоцитоз
ORPHA:280785· ICD-10 Q82.2· Bullous diffuse cutaneous mastocytosis
Визначення(English summary)
Bullous diffuse cutaneous mastocytosis (BDCM) is a form of diffuse cutaneous mastocytosis (DCM; see this term) characterized by generalized erythroderma and severe blistering associated with the accumulation of mast cells in the skin.
- Поширеність
- <1 / 1 000 000
- Успадкування
- Not applicable
- Вік початку
- Infancy, Neonatal