Гостра некротизуюча енцефалопатія дитячого віку
ORPHA:263524· ICD-10 G31.8· Acute necrotizing encephalopathy of childhood
Визначення(English summary)
A rare neurologic disease characterized by a rapid onset of seizures, an altered state of consciousness, neurologic decline, and variable degrees of hepatic dysfunction following a respiratory or gastrointesitnal infection (e.g. mycoplasma, influenza virus) in a previously healthy child. Brain MRI of patients reveals bilateral, multiple, symmetrical lesions predominantly observed in thalami and brainstem, but also in periventricular white matter and cerebellum in some cases.
- Поширеність
- Unknown
- Успадкування
- Not applicable
- Вік початку
- Childhood