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Пізній вогнищевий дермальний еластоз

ORPHA:228227· ICD-10 L98.8· Late-onset focal dermal elastosis

Визначення(English summary)

Late-onset focal dermal elastosis is a rare, acquired, dermis elastic tissue disorder characterized by a pseudoxanthoma elasticum-like papular eruption consisting of multiple, slowly progressive, asymptomatic, 2-5 mm, white to yellowish, non-follicular papules (that tend to form cobblestone plaques) predominantly distributed over the neck, axillae and flexural areas, with no systemic involvement. Skin biopsy reveals a focal increase of normal-appearing elastic tissue in the reticular dermis with no calcium deposits.

Поширеність
<1 / 1 000 000
Успадкування
Not applicable
Вік початку
Adult