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Дифузний гіперінсулінізм, резистентний до діазоксиду

ORPHA:165988· Diazoxide-resistant diffuse hyperinsulinism

Визначення(English summary)

Diazoxide-resistant diffuse hyperinsulism (DRDH) is a form of Diazoxide resistant hyperinsulinism (see this term) characterized by recurrent episodes of profound hypoglycemia caused by an excessive/ uncontrolled insulin secretion (inappropriate for the level of glycemia) due to diffuse involvement of pancreas that is unresponsive to medical treatment with diazoxide, often necessitating near total/total pancreatectomy.