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Одношлуночкове серце

ORPHA:1464· ICD-10 Q20.4· Univentricular heart

Визначення(English summary)

A severe congenital cardiac malformation characterized by both atria related entirely or almost entirely to one functionally single ventricular chamber. The clinical manifestations include congestive heart failure, failure to thrive, cyanosis, hypoxemia and neurodevelopmental disabilities.

Поширеність
1-9 / 100 000
Успадкування
Not applicable
Вік початку
Infancy, Neonatal