Univentricular heart
ORPHA:1464· ICD-10 Q20.4
Definition
A severe congenital cardiac malformation characterized by both atria related entirely or almost entirely to one functionally single ventricular chamber. The clinical manifestations include congestive heart failure, failure to thrive, cyanosis, hypoxemia and neurodevelopmental disabilities.
- Prevalence
- 1-9 / 100 000
- Inheritance
- Not applicable
- Age of onset
- Infancy, Neonatal