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Вроджений панфолікулярний невус

ORPHA:139414· ICD-10 I78.1· Congenital panfollicular nevus

Визначення(English summary)

Congenital panfollicular nevus is a rare, benign, skin tumor disorder characterized by the presence of congenital, large (few centimeters), elevated, well-circumscribed, pink-tan, multinodular, non-ulcerative, bosselated-surface skin lesions located on the neck, scalp or hand and which enlarge with time. Histologically, hamartomatous proliferation containing irregularly arranged, malformed hair follicles in various stages of development, surrounded by fibrous tissue and densely distributed within the dermis is observed.

Поширеність
<1 / 1 000 000
Вік початку
Infancy, Neonatal