Хвороба Бехчета
ORPHA:117· ICD-10 M35.2· Behçet disease
Визначення(English summary)
A rare, chronic, relapsing, multisystemic vasculitis characterized by mucocutaneous lesions, as well as articular, vascular, ocular and central nervous system manifestations.
- Поширеність
- 1-9 / 1 000 000
- Успадкування
- Multigenic/multifactorial
- Вік початку
- Adolescent, Adult, Childhood