Behçet disease
ORPHA:117· ICD-10 M35.2
Definition
A rare, chronic, relapsing, multisystemic vasculitis characterized by mucocutaneous lesions, as well as articular, vascular, ocular and central nervous system manifestations.
- Prevalence
- 1-9 / 1 000 000
- Inheritance
- Multigenic/multifactorial
- Age of onset
- Adolescent, Adult, Childhood