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Van der Woude syndrome

ORPHA:888· ICD-10 Q38.0

Definition

Van der Woude syndrome (VWS) is a rare congenital genetic dysmorphic syndrome characterized by paramedian lower-lip fistulae, cleft lip with or without cleft palate, or isolated cleft palate.

Prevalence
1-9 / 100 000
Inheritance
Autosomal dominant, Not applicable
Age of onset
Antenatal, Neonatal