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Gaucher disease

ORPHA:355· ICD-10 E75.2

Definition

Gaucher disease (GD) is a lysosomal storage disorder encompassing three main forms (types 1, 2 and 3), a fetal form and a variant with cardiac involvement (Gaucher disease - ophthalmoplegia - cardiovascular calcification or Gaucher-like disease).

Prevalence
1-9 / 100 000
Inheritance
Autosomal recessive
Age of onset
All ages