vitalwiki

Adult familial nephronophthisis-spastic quadriparesia syndrome

ORPHA:2666· ICD-10 Q61.8

Definition

A rare, genetic, renal disease characterized by the association of familial adult medullary cystic disease with spastic quadriparesis. There have been no further descriptions in the literature since 1990.

Prevalence
<1 / 1 000 000
Inheritance
Unknown
Age of onset
Adult