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Autosomal recessive sideroblastic anemia

ORPHA:260305· ICD-10 D64.0

Definition

Congenital autosomal recessive sideroblastic anemia (ARSA) is a non-syndromic, microcytic/hypochromic sideroblastic anemia, present from early infancy and characterized by severe microcytic anemia, which is not pyridoxine responsive, and increased serum ferritin.

Inheritance
Autosomal recessive
Age of onset
Infancy, Neonatal