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Lennox-Gastaut syndrome

ORPHA:2382· ICD-10 G40.4

Definition

A rare, severe early-onset developmental epileptic encephalopathy characterized by the triad of intellectual impairment, multiple seizure types, and typical electroencephalography (EEG) abnormalities.

Prevalence
1-9 / 1 000 000
Inheritance
Autosomal dominant, Multigenic/multifactorial, Not applicable
Age of onset
Childhood, Infancy