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Familial generalized lentiginosis

ORPHA:231040· ICD-10 L81.4

Definition

Familial generalized lentiginosis is a rare, inherited, skin hyperpigmentation disorder characterized by widespread lentigines without associated noncutaneous abnormalities. Patients present multiple brown to dark brown, non-elevated macula of 0.2 to 1 cm in diameter, spread over the entire body, sometimes including palms or soles, but never oral mucosa.

Prevalence
Unknown
Inheritance
Autosomal dominant, Unknown
Age of onset
All ages