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Craniodiaphyseal dysplasia

ORPHA:1513· ICD-10 M85.2

Definition

Craniodiaphyseal dysplasia is a rare sclerotic bone disorder with a variable phenotypic expression with massive generalized hyperostosis and sclerosis, particularly of the skull and facial bones, that may lead to severe deformity.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant, Autosomal recessive, Not applicable
Age of onset
Childhood