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Bilateral microtia-deafness-cleft palate syndrome

ORPHA:140963· ICD-10 Q87.0

Definition

A rare genetic, orofacial clefting syndrome characterized by the association of bilateral microtia with severe to profound hearing impairment, and cleft palate.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant, Autosomal recessive
Age of onset
Neonatal