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Aplasia cutis congenita

ORPHA:1114· ICD-10 Q84.8

Definition

A rare skin disorder characterized by localized absence of skin that is usually located on the scalp but can occur anywhere on the body including the face, trunk and extremities. Aplasia cutis congenita (ACC) may occasionally be associated with other anomalies.

Prevalence
1-5 / 10 000
Inheritance
Autosomal dominant, Autosomal recessive, Not applicable
Age of onset
Antenatal, Neonatal