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Autosomal dominant palmoplantar keratoderma and congenital alopecia

ORPHA:1010· ICD-10 Q82.8

Definition

A rare genetic skin disorder characterized by absence of scalp and body hair and palmoplantar keratoderma, without other hand complications.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant
Age of onset
Infancy, Neonatal