Мастоцитарна лейкемія
ORPHA:98851· ICD-10 C94.3· Mast cell leukemia
Визначення(English summary)
A very rare malignant systemic mastocytosis (SM) characterized by a huge infiltration of bone marrow, and often of blood, by abnormal mast cells (MC) which frequently manifests with organ dysfunction (liver, spleen, peritoneum, bones, and marrow).
- Поширеність
- <1 / 1 000 000
- Успадкування
- Not applicable
- Вік початку
- All ages