Mast cell leukemia
ORPHA:98851· ICD-10 C94.3
Definition
A very rare malignant systemic mastocytosis (SM) characterized by a huge infiltration of bone marrow, and often of blood, by abnormal mast cells (MC) which frequently manifests with organ dysfunction (liver, spleen, peritoneum, bones, and marrow).
- Prevalence
- <1 / 1 000 000
- Inheritance
- Not applicable
- Age of onset
- All ages