Меланома мяких тканин
ORPHA:97338· ICD-10 C43.6· Melanoma of soft tissue
Визначення(English summary)
A rare soft tissue tumor characterized by a slowly growing mass typically involving tendons and aponeuroses of the extremities, composed of polygonal or spindle-shaped cells with melanocytic differentiation. The tumor typically affects young adults, who often present with pain or tenderness at the tumor site. Prognosis is poor with high recurrence rates and frequent metastasis, especially to lymph nodes, lung, and bones.
- Поширеність
- 1-9 / 100 000
- Успадкування
- Not applicable
- Вік початку
- Adult