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Melanoma of soft tissue

ORPHA:97338· ICD-10 C43.6

Definition

A rare soft tissue tumor characterized by a slowly growing mass typically involving tendons and aponeuroses of the extremities, composed of polygonal or spindle-shaped cells with melanocytic differentiation. The tumor typically affects young adults, who often present with pain or tenderness at the tumor site. Prognosis is poor with high recurrence rates and frequent metastasis, especially to lymph nodes, lung, and bones.

Prevalence
1-9 / 100 000
Inheritance
Not applicable
Age of onset
Adult