Синдром Айзенменгера
ORPHA:97214· ICD-10 I27.2· Eisenmenger syndrome
Визначення(English summary)
A rare respiratory disease associated with unoperated congenital heart disease and characterized by congenital heart malformations with reversed or bi-directional shunting through an intra-cardiac or intervascular (usually aorto-pulmonary) communication with the development of PAH.
- Поширеність
- 1-9 / 1 000 000
- Успадкування
- Not applicable
- Вік початку
- Adolescent, Adult, Childhood