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Задній уретральний клапан

ORPHA:93110· ICD-10 Q64.2· Posterior urethral valve

Визначення(English summary)

A rare, congenital, fetal lower urinary tract obstruction (LUTO) anomaly characterized by an abnormal congenital obstructing membrane or leaflets that are located within the posterior urethra associated with significant obstruction of the male bladder restricting normal bladder emptying.

Поширеність
1-9 / 100 000
Успадкування
Autosomal recessive, Not applicable, X-linked recessive
Вік початку
All ages