vitalwiki

Posterior urethral valve

ORPHA:93110· ICD-10 Q64.2

Definition

A rare, congenital, fetal lower urinary tract obstruction (LUTO) anomaly characterized by an abnormal congenital obstructing membrane or leaflets that are located within the posterior urethra associated with significant obstruction of the male bladder restricting normal bladder emptying.

Prevalence
1-9 / 100 000
Inheritance
Autosomal recessive, Not applicable, X-linked recessive
Age of onset
All ages