Вторинна кишкова лімфангіектазія
ORPHA:90363· ICD-10 I89.0· Secondary intestinal lymphangiectasia
Визначення(English summary)
Secondary intestinal lymphangiectasia is an acquired from of intestinal lymphangiectasia (see this term) manifesting as a protein-losing enteropathy due to another disorder such as Crohns disease, congestive heart failure, sarcoidosis, Turner syndrome (see these terms) and often in patients who have undergone a Fontan operation. It is characterized by malabsorption, diarrhea, edema due hypoproteinemia, steatorrhea and serosal effusions.
- Вік початку
- Adult, Elderly