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Лімфома маргінальної зони селезінки

ORPHA:86854· ICD-10 C83.0· Splenic marginal zone lymphoma

Визначення(English summary)

Splenic marginal zone lymphoma is a rare, indolent B-cell non-Hodgkin lymphoma characterized by abnormal clonal proliferation of mature B-lymphocytes with involvement in the spleen, bone marrow and, frequently, the blood. It usually presents with splenomegaly, lymphocytosis, anemia and/or thrombocytopenia. Hepatitis C virus and autoimmune manifestations, such as autoimmune hemolytic anemia and autoimmune thrombocytopenia, could be associated.

Поширеність
1-9 / 1 000 000
Успадкування
Not applicable
Вік початку
Adult