Десмопластична невелика круглоклітинна пухлина
ORPHA:83469· ICD-10 C48.2· Desmoplastic small round cell tumor
Визначення(English summary)
An aggressive soft tissue cancer that typically arises in serous lined surfaces of the abdominal or pelvic peritoneum, and spreads to the omentum, lymph nodes and hematogenously disseminates especially to the liver. Extraserous primary location has been reported in exceptional cases.
- Поширеність
- <1 / 1 000 000
- Успадкування
- Not applicable
- Вік початку
- Adolescent, Adult