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Комплекс туберозного склерозу

ORPHA:805· ICD-10 Q85.1· Tuberous sclerosis complex

Визначення(English summary)

A rare neurocutaneous disorder characterized by multisystem hamartomas, most commonly involving the skin, brain, kidneys, lungs, eye, and heart, and associated with neuropsychiatric disorders.

Поширеність
1-9 / 100 000
Успадкування
Autosomal dominant
Вік початку
All ages