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Tuberous sclerosis complex

ORPHA:805· ICD-10 Q85.1

Definition

A rare neurocutaneous disorder characterized by multisystem hamartomas, most commonly involving the skin, brain, kidneys, lungs, eye, and heart, and associated with neuropsychiatric disorders.

Prevalence
1-9 / 100 000
Inheritance
Autosomal dominant
Age of onset
All ages