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Саркоїдоз

ORPHA:797· ICD-10 D86.0· Sarcoidosis

Визначення(English summary)

A rare multisystemic, autoinflammatory disorder of unknown etiology characterized by the formation of immune, non-caseating granulomas in any organ(s), leading to variable clinical symptoms and severity. Clinical presentation is typically with persistent dry cough, eye or skin manifestations, peripheral lymph nodes, fatigue, weight loss, fever or night sweats, and Löfgren syndrome.

Поширеність
1-5 / 10 000
Успадкування
Multigenic/multifactorial
Вік початку
Adolescent, Adult, Childhood, Elderly