Пемфігоїд рубцевий
ORPHA:79481· ICD-10 L10.2· Pemphigus foliaceus
Визначення(English summary)
A rare superficial pemphigus disease characterized by multiple, pruritic, scaly, crusted cutaneous erosions, with flaky circumscribed patches, localized mostly on the face, scalp, trunk and extremities, often presenting an erythematous base. Mucosal involvement is rarely observed.
- Поширеність
- 1-9 / 100 000
- Вік початку
- All ages