Pemphigus foliaceus
ORPHA:79481· ICD-10 L10.2
Definition
A rare superficial pemphigus disease characterized by multiple, pruritic, scaly, crusted cutaneous erosions, with flaky circumscribed patches, localized mostly on the face, scalp, trunk and extremities, often presenting an erythematous base. Mucosal involvement is rarely observed.
- Prevalence
- 1-9 / 100 000
- Age of onset
- All ages