Інтерстиціальний гранулематозний дерматит з артритом
ORPHA:79099· ICD-10 L30.8· Interstitial granulomatous dermatitis with arthritis
Визначення(English summary)
Interstitial granulomatous dermatitis with arthritis is a rare rheumatologic disease characterized by the occurrence of inflammatory arthritis in association with large, erythematous, symmetrical cutaneous lesions (ranging from typical, but infrequent, cord-like lesions on the flanks to more common violaceous plaques on the trunk and limbs) featuring a typical histologic infiltrate mainly constituted of histiocytes.
- Поширеність
- <1 / 1 000 000
- Успадкування
- Not applicable
- Вік початку
- Adult