Поліцитемія стправжня
ORPHA:729· ICD-10 D45· Polycythemia vera
Визначення(English summary)
Polycythemia vera (PV) is an acquired myeloproliferative disorder characterized by an elevated absolute red blood cell mass caused by uncontrolled red blood cell production, frequently associated with uncontrolled white blood cell and platelet production.
- Поширеність
- 1-9 / 100 000
- Успадкування
- Not applicable
- Вік початку
- All ages