Polycythemia vera
ORPHA:729· ICD-10 D45
Definition
A rare acquired myeloproliferative neoplasm characterized by an elevated absolute red blood cell mass (RBCM) caused by uncontrolled red blood cell production, frequently associated with uncontrolled white blood cell and platelet production.
- Prevalence
- 1-9 / 100 000
- Inheritance
- Not applicable
- Age of onset
- All ages