Ідіопатичний бронхоектаз
ORPHA:60033· ICD-10 J47· Idiopathic bronchiectasis
Визначення(English summary)
Idiopathic bronchiectasis (IB) is a progressive lung disease characterized by chronic dilation of the bronchi and destruction of the bronchial walls in the absence of any underlying cause (such as post infectious disease, aspiration, immunodeficiency, congenital abnormalities and ciliary anomalies).
- Поширеність
- 1-9 / 100 000
- Успадкування
- Not applicable
- Вік початку
- All ages