Idiopathic bronchiectasis
ORPHA:60033· ICD-10 J47
Definition
Idiopathic bronchiectasis (IB) is a progressive lung disease characterized by chronic dilation of the bronchi and destruction of the bronchial walls in the absence of any underlying cause (such as post infectious disease, aspiration, immunodeficiency, congenital abnormalities and ciliary anomalies).
- Prevalence
- 1-9 / 100 000
- Inheritance
- Not applicable
- Age of onset
- All ages